Can congenital pulmonary airway malformation be distinguished from Type I pleuropulmonary blastoma based on clinical and radiological features?
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چکیده
منابع مشابه
It's Rare So Be Aware: Pleuropulmonary Blastoma Mimicking Congenital Pulmonary Airway Malformation
Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood. The tumor arises in the lung and pleura and is regarded as a pulmonary dysontogenetic or embryonic neoplasm. Four types are defined in literature. Type I PPB is a rare, cystic lung neoplasm in infants characterized by subtle malignant changes and a good prognosis. Recurrences after type I PPB are...
متن کاملFGF10 Signaling differences between type I pleuropulmonary blastoma and congenital cystic adenomatoid malformation
BACKGROUND Type I pleuropulmonary blastoma (PPB) and congenital cystic adenomatoid malformation of the lung (CCAM) are cystic lung diseases of childhood. Their clinical and radiological presentations are often similar, and pathologic discrimination remains difficult in many cases. As a consequence, type I PPB and CCAM are frequently confused, leading to delayed adequate management for type I PP...
متن کاملPleuropulmonary blastoma: transition from type I (cystic) to type III (solid).
Pleuropulmonary blastoma is a unique dysontogenetic neoplasm of childhood that appears as a pulmonary and/or pleural-based mass, and is characterised histologically by a primitive, variably mixed blastematic and sarcomatous appearance. We report a 12-month-old female child who was operated for a lung cyst at the age of six months and postoperative histopathology was suggestive of type I pleurop...
متن کاملType II- Pleuropulmonary Blastoma: A case report
Pleuropulmonary blastoma is a rare and aggressive neoplasm typically presents in young children, younger than 5 years, as a pulmonary and/or pleural-based tumor. We reported a case of type-II pleuropulmonary blastoma (PPB) in an 8 month old infant who presented to Al-Khansa'a Maternity Hospital in Western Mosul with a history of repeated attacks of shortness of breath and signs of pulmonary inf...
متن کاملCongenital Pulmonary Airway Malformation Type 4: A Case Report
Congenital pulmonary airway malformation (CPAM) is a very rare pulmonary disease in children. It is often misdiagnosed as a persistent and localized pneumothorax without any further pathological diagnosis. Malignancy and frequent airway infections are major concerns in these patients. Surgical excision is recommended to make a definite diagnosis and exclude hidden malignancies, and is also the ...
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ژورنال
عنوان ژورنال: Journal of Pediatric Surgery
سال: 2016
ISSN: 0022-3468
DOI: 10.1016/j.jpedsurg.2015.10.019